Figure 1

Audiometric tracings prior to CI in 10 patients with MYH9 -RD. Each audiogram reports the air conduction hearing thresholds of the analyzed patients. Patients are identified by numbers on top right, which correspond to identification numbers reported in Tables. Hearing threshold is defined as the minimum sound intensity (presented at different frequencies) that can be still perceived by the individual during the audiometric examination. Hearing thresholds were measured in decibel hearing level (dB HL) and frequencies ranged from 0.25 to 8 kHz. The right ear is indicated by the red symbol “O” and the left ear by the blue symbol “X”. Severe deafness is defined by mean hearing thresholds worse than 70 dB HL, profound deafness by mean hearing thresholds worse than 90 dB HL. Arrows indicate hearing thresholds worse than 120 dB HL.