From: Aggressive mature natural killer cell neoplasms: from epidemiology todiagnosis
WHO classification, 2008 | Disease entities | Putative cells of origin | Orphanet numbers | Synonyms in the Orphanet data base | ICD codes | Prevalence categories (/1.000.000) | [References] | |
---|---|---|---|---|---|---|---|---|
 |  |  |  |  | ICD-10 | ICD-O-3 |  |  |
NK-cell neoplasms | Extranodal NK/T-cell lymphoma (NKTCL), nasal type | Mature NK-cells | 86879 | NK/T-cell lymphoma; Nasal T/natural killer-cell lymphoma;Angiocentric T-cell lymphoma; Lethal midline granuloma | C86.0 | 9719/3 | <1-9 | |
Aggressive NK-cell leukemia (ANKCL) | Mature NK-cells | 86873 | Aggressive NK-cell leukemia; Aggressive NK-cell lymphoma; NK-cellLGL leukemia; NK-cell large granular lymphocyte leukemia | C94.7 | 9948/3 | <1-9 | ||
Provisional entities | Chronic lymphoproliferative disorders of NK-cells (CLPD-NK) | Mature NK-cells | Not available | NK-cell LGL leukemia; NK-cell large granular lymphocyte leukemia(considered together with ANKCL) | Not available (C94.7)* | Not available (9831/3)** | Unknown | |
 | NK-cell lymphoblastic leukemia / lymphoma | NK-, T- and/or myeloid precursor cells | Not available | Not available | Not available | Not available | Unknown |