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Table 2 Patient demographic and baseline characteristics in 4 patients ≥19 years of age

From: Assessment of bone mineral density by dual energy x-ray absorptiometry in patients with mucopolysaccharidoses

MPS type n Age (yr) Age range (yr) Height z score Weight z score BMI z score BMD (g/cm2) BMD T-score
MPS I (H/S*) 1 22.5 22.5 −6.38 −3.31 −1.58 0.614 −3.49
MPS II 2 22.6 (1.6) 21.5-23.7 −9.15 (0.33) −2.54 (0.12) 0.47 (0.1) 0.64 (0.006) −6.6 (0.07)
MPS VI 1 22.8 22.8 −8.88 −3.25 −0.11 0.712 −2.82
Total 4 22.6 (0.9) 21.5-23.7 −8.39 (1.36) −2.91 (0.43) −0.19 (0.97) 0.65 (0.04) −4.88 (2.01)
  1. Values are displayed as mean (standard deviation).
  2. MPS, mucopolysaccharidoses; H/S*, Hurler/Scheie; z score, standard deviation score; BMI, body mass index; BMD, bone mineral density; HAZ, height-for-age z score.