Skip to main content

Table 2 Patient demographic and baseline characteristics in 4 patients ≥19 years of age

From: Assessment of bone mineral density by dual energy x-ray absorptiometry in patients with mucopolysaccharidoses

MPS type

n

Age (yr)

Age range (yr)

Height z score

Weight z score

BMI z score

BMD (g/cm2)

BMD T-score

MPS I (H/S*)

1

22.5

22.5

−6.38

−3.31

−1.58

0.614

−3.49

MPS II

2

22.6 (1.6)

21.5-23.7

−9.15 (0.33)

−2.54 (0.12)

0.47 (0.1)

0.64 (0.006)

−6.6 (0.07)

MPS VI

1

22.8

22.8

−8.88

−3.25

−0.11

0.712

−2.82

Total

4

22.6 (0.9)

21.5-23.7

−8.39 (1.36)

−2.91 (0.43)

−0.19 (0.97)

0.65 (0.04)

−4.88 (2.01)

  1. Values are displayed as mean (standard deviation).
  2. MPS, mucopolysaccharidoses; H/S*, Hurler/Scheie; z score, standard deviation score; BMI, body mass index; BMD, bone mineral density; HAZ, height-for-age z score.