MPS type | n | Age (yr) | Age range (yr) | Height z score | Weight z score | BMI z score | BMD (g/cm2) | BMD T-score |
---|---|---|---|---|---|---|---|---|
MPS I (H/S*) | 1 | 22.5 | 22.5 | −6.38 | −3.31 | −1.58 | 0.614 | −3.49 |
MPS II | 2 | 22.6 (1.6) | 21.5-23.7 | −9.15 (0.33) | −2.54 (0.12) | 0.47 (0.1) | 0.64 (0.006) | −6.6 (0.07) |
MPS VI | 1 | 22.8 | 22.8 | −8.88 | −3.25 | −0.11 | 0.712 | −2.82 |
Total | 4 | 22.6 (0.9) | 21.5-23.7 | −8.39 (1.36) | −2.91 (0.43) | −0.19 (0.97) | 0.65 (0.04) | −4.88 (2.01) |