Skip to main content

Table 1 Patient demographic and baseline characteristics in 26 patients <19 years of age

From: Assessment of bone mineral density by dual energy x-ray absorptiometry in patients with mucopolysaccharidoses

MPS type n Age (yr) Age range (yr) Height z score Weight z score BMI z score BMD z score HAZ adjusted BMD z score
MPS I (H/S*) 1 18.5 18.5 −7.69 −2.13 0.53 −6.51 −1.18
MPS II 10 11.1 (5.2) 5-18.4 −3.05 (1.84) −0.19 (1.76) 1.06 (1.37) −2.34 (1.45) −0.61 (1.32)
MPS IIIB 2 7.2 (0) 7.2 −0.56 (0.06) 0.36 (0) 1 (0.05) −0.93 (0.17) −0.78 (0.20)
MPS IVA 9 10.1 (3.2) 5.8-15.3 −6.54 (2.21) −2.27 (0.81) 0.36 (1.47) −4.08 (0.88) −0.89 (1.29)
MPS VI 4 9.1 (2.1) 6.6-11.7 −4.90 (1.52) −1.50 (0.31) 0.72 (0.59) −2.57 (1.15) −0.33 (1.63)
Total 26 10.4 (4.2) 5-18.5 −4.53 (2.66) −1.15 (1.55) 0.74 (1.23) −3.03 (1.62) −0.70 (1.24)
  1. Values are displayed as mean (standard deviation).
  2. MPS, mucopolysaccharidoses; H/S*, Hurler/Scheie; z score, standard deviation score; BMI, body mass index; BMD, bone mineral density; HAZ, height-for-age z score.