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Table 1 Patient demographic and baseline characteristics in 26 patients <19 years of age

From: Assessment of bone mineral density by dual energy x-ray absorptiometry in patients with mucopolysaccharidoses

MPS type

n

Age (yr)

Age range (yr)

Height z score

Weight z score

BMI z score

BMD z score

HAZ adjusted BMD z score

MPS I (H/S*)

1

18.5

18.5

−7.69

−2.13

0.53

−6.51

−1.18

MPS II

10

11.1 (5.2)

5-18.4

−3.05 (1.84)

−0.19 (1.76)

1.06 (1.37)

−2.34 (1.45)

−0.61 (1.32)

MPS IIIB

2

7.2 (0)

7.2

−0.56 (0.06)

0.36 (0)

1 (0.05)

−0.93 (0.17)

−0.78 (0.20)

MPS IVA

9

10.1 (3.2)

5.8-15.3

−6.54 (2.21)

−2.27 (0.81)

0.36 (1.47)

−4.08 (0.88)

−0.89 (1.29)

MPS VI

4

9.1 (2.1)

6.6-11.7

−4.90 (1.52)

−1.50 (0.31)

0.72 (0.59)

−2.57 (1.15)

−0.33 (1.63)

Total

26

10.4 (4.2)

5-18.5

−4.53 (2.66)

−1.15 (1.55)

0.74 (1.23)

−3.03 (1.62)

−0.70 (1.24)

  1. Values are displayed as mean (standard deviation).
  2. MPS, mucopolysaccharidoses; H/S*, Hurler/Scheie; z score, standard deviation score; BMI, body mass index; BMD, bone mineral density; HAZ, height-for-age z score.