MPS type | n | Age (yr) | Age range (yr) | Height z score | Weight z score | BMI z score | BMD z score | HAZ adjusted BMD z score |
---|---|---|---|---|---|---|---|---|
MPS I (H/S*) | 1 | 18.5 | 18.5 | −7.69 | −2.13 | 0.53 | −6.51 | −1.18 |
MPS II | 10 | 11.1 (5.2) | 5-18.4 | −3.05 (1.84) | −0.19 (1.76) | 1.06 (1.37) | −2.34 (1.45) | −0.61 (1.32) |
MPS IIIB | 2 | 7.2 (0) | 7.2 | −0.56 (0.06) | 0.36 (0) | 1 (0.05) | −0.93 (0.17) | −0.78 (0.20) |
MPS IVA | 9 | 10.1 (3.2) | 5.8-15.3 | −6.54 (2.21) | −2.27 (0.81) | 0.36 (1.47) | −4.08 (0.88) | −0.89 (1.29) |
MPS VI | 4 | 9.1 (2.1) | 6.6-11.7 | −4.90 (1.52) | −1.50 (0.31) | 0.72 (0.59) | −2.57 (1.15) | −0.33 (1.63) |
Total | 26 | 10.4 (4.2) | 5-18.5 | −4.53 (2.66) | −1.15 (1.55) | 0.74 (1.23) | −3.03 (1.62) | −0.70 (1.24) |