Figure 1From: In vitro and in vivo consequences of variant medium-chain acyl-CoA dehydrogenase genotypesResidual MCAD enzyme activities measured with different substrates in leukocytes. A: Residual MCAD enzyme activities measured with C6-CoA; B: Residual MCAD enzyme activities measured with C6-CoA+C4-CoA; C: Residual MCAD enzyme activities measured with PP-CoA; D: MCAD enzyme activity with PP-CoA correlates with the effect of C4-CoA on C6-CoA enzyme activity. Enzyme activity measured with C6-CoA is set at 100% on the y-axis. Residual MCAD enzyme activities are depicted as percentage from controls. At least one control was included in each enzyme assay. Medians are indicated. * p<0.05; ** p<0.001.Back to article page