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Table 1 Surface immunophenotype of stem cells isolated from skin biopsies or culture fibroblasts

From: A human neuronal model of Niemann Pick C disease developed from stem cells isolated from patient’s skin

 

Healthy donor (skin biopsy)

NP-C (skin biopsy)

Healthy donor (fibroblast culture)

NP-C (fibroblast culture)

CD49d

95.9 ± 3.2

99.89 ± 0.22

99.1 ± 0.7

99.9 ± 0.08

CD49a

37.5 ± 7.2

48.6 ± 0.4

6.38 ± 2.51

54.18 ± 3.44

CD49b

96.48 ± 2.8

99.21 ± 0.3

99.98 ± 0.1

99.95 ± 0.2

CD29

43.33 ± 12.5

62.75 ± 1.05

17.05 ± 14.7

17.62 ± 4.9

ABCG2

1.57 ± 0.7

1.14 ± 0.02

1.81 ± 0.06

1.37 ± 0.25

CXCR4

0.22 ± 0.1

0.16 ± 0.01

0.081 ± 0.06

0.18 ± 0.05

CD10

77.8 ± 13

98 ± 0.4

55.5 ± 20.7

96.05 ± 1.2

CD66

1.23 ± 0.7

3.04 ± 0.05

0.72 ± 0.7

0.28 ± 0.23

CD133

2.06 ± 0.34

5.88 ± 0.28

0.31 ± 0.08

0.23 ± 0.12

CD271

2.95 ± 1.33

0.2 ± 0.071

0.37 ± 0.31

0.89 ± 0.24

CD44

95.89 ± 2.7

97.25 ± 0.2

99.41 ± 0.7

98.94 ± 1.02

CD105

87 ± 3.4

85.9 ± 2.78

92.73 ± 4.35

74.92 ± 30.8

CD90

97.12 ± 3.2

98.88 ± 1.41

99.52 ± 0.28

96.25 ± 3.7

CD73

92.9 ± 3.7

99.75 ± 0.08

99.48 ± 0.4

99.7 ± 0.19

CD34

3.7 ± 1.7

1.9 ± 0.1

0.205 ± 0.12

0.66 ± 0.83

CD45

0.1 ± 0.2

0.19 ± 0.01

0.45 ± 0.04

0.07 ± 0.02

KDR

3.12 ± 1.1

1.47 ± 0.03

1.92 ± 2.18

1.53 ± 0.18

CD13

98.49 ± 3.7

98.4 ± 1.9

99.78 ± 0.21

99.88 ± 0.15

CD117

1.1 ± 0.67

0.52 ± 0.03

0.15 ± 0.13

0.27 ± 0.3

HLA-DR

0.37 ± 0.1

0.12 ± 0.14

0.65 ± 1.01

0.03 ± 0.01