Symptoms before diagnosis | MPS Subtype (N°) | N° casos | Median | |||
---|---|---|---|---|---|---|
A | B | C | Age | |||
(Range) | ||||||
Coarse facial features | 24 | 9 | 9 | 42 | 78% | 3 years |
( 1 – 4 y) | ||||||
Recurrent diarrhea | 17 | 4 | 6 | 27 | 50% | 2 years |
(1 – 4.5 y) | ||||||
Umbilical hernia | 7 | 4 | 1 | 12 | 22% | 1 months |
(0 – 8 months) | ||||||
Inguinal hernia | 4 | 0 | 0 | 4 | 7% | 1,6 year |
( 0–3 y) | ||||||
Recurrent otitis | 15 | 5 | 5 | 25 | 46% | 1 year |
(0–3.5 y) | ||||||
Hearing loss | 12 | 2 | 6 | 11 | 30% | 2.2 year |
(1.5 – 6 y) | ||||||
Adenoidectomy | 14 | 2 | 7 | 23 | 43% | 3 year |
(2 – 6 y) | ||||||
Tonsillectomy | 8 | 3 | 4 | 15 | 28% | 3.8 year |
(2 – 9 y) | ||||||
Speech delayed | 27 | 11 | 8 | 46 | 85% | 3 year |
(2.5 – 7 y) | ||||||
Hyperactivity | 21 | 6 | 8 | 35 | 65% | 3 year |
(1.5 – 10 y) | ||||||
Sleep disorders | 14 | 5 | 5 | 24 | 44% | 1 year |
( 2 months -6 y) |