From: A prospective observational study of associated anomalies in Hirschsprung’s disease
Syndromic, n (%, 95%CI) | Non-syndromic, n (%, 95% CI) | p | |
---|---|---|---|
Patients, n | 10 (9%, 5%-16%) | 96 (91%, 83%-95%) | |
Median age | 2,25 | 2,42 | n.a. |
Male to female ratio | 2,33:1 | 3,57:1 | 0,6912 |
S-HSCR | 6 (60%, 31%-83%) | 73 (76%, 67%-83%) | 0,2719 |
Other HSCR forms | 4 (40%, 17%-69%) | 23 (24%, 16%-33%) | |
VI | 6 (60%, 31%-83%) | 40 (41,7) | 0,7918 |
CAKUT | 4 (40%, 17%-69%) | 18 (18,7) | 0,2106 |
CHD | 5 (50%, 24%-76%) | 0 (0%, 0%-5%) | 0,0001 |
HI | 1 (10%, 18%-40%) | 4 (4%, 2%-10%) | 0,3968 |
CNS anomalies | 0 (0%, 0%-33%) | 1 (1%, 0,2%-57%) | 1,000 |
OTHER | 3 (30%, 11%-60%) | 10 (10%, 6%-18%) | 0,1044 |