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Table 2 Ocular and neurological characteristics of patients with juvenile parenchymal Neuro-Behçet reported in the literature from 1971 to 2011

From: Neuro-Behçet’s disease in childhood: A focus on the neuro-ophthalmological features

Patient

Author [Ref.]

OCULAR

NEUROLOGICAL

  

Signs

Symptoms

Signs

Symptoms

1

Mitra [33]

Papilledema

Blurry vision Diplopia

Aseptic meningitis

Headache

Cranial nerve palsies

2

Vignola [34]

Retinal vasculitis

-

Aseptic meningitis

Seizure

3

Saltik [38]

Nystagmus Uveitis

Diplopia

Cranial nerve palsies

Headache

Encephalomyelitis

Hemiparesis

4

Hatachi [41]

Nystagmus Uveitis

-

Aseptic meningitis

Fever

Cranial nerve palsies

Headache

Hearing impairment

Vertigo

Vomiting

5

Kara [42]

Papilledema Retinal vasculitis

-

Aseptic meningitis

Fever

Headache

Vomiting

6

Pipitone [46]

Papillitis (bilateral)

-

Encephalomyelitis

Headache

Retinal vasculitis

 

7

Robinson [47]

Papillitis (unilateral)

Blurry vision

Encephalomyelitis

Seizure

Vertigo

8

Metreau-Vastel [48]

-

-

Ataxia

Lapse in concentration

Hemiparesis

Meningoencephalitis

9

Metreau-Vastel [48]

-

Blurry vision

Ataxia

-

Hemiparesis

 

Rhombencephalitis

10

Metreau-Vastel [48]

-

-

Rhombencephalitis

Behaviour problems

Lapse in concentration

Loss of memory

11

Metreau-Vastel [48]

-

-

Trasverse Myelitis

Mental retardation

Seizure

14* (3 cases)

Uluduz [14]

-

-

Relapsing Myelitis (1)

Headache (1)

Hemiparesis (3)

Seizure (3)