Clinical characteristics of patients with spinocerebellar ataxias 1, 2, 3 and 6 in the US; a prospective observational study

Table 1 Baseline clinical characteristics and the increase in SARA Total Score estimated from the baseline score and the duration of the disease

			Age at onset (yrs)		Age at baseline (yrs)		Duration of disease (yrs)		SARA Total Score		Annual estimated increase in SARA Total Score	Standard error of parameter estimate	R²	R
Type of SCA	N	M/F	Mean	STD	Mean	STD	Mean	STD	Mean	STD
SCA1	60	0.79	40.41	11.40	49.28	12.64	8.93	6.89	14.16	8.39	1.2385	0.0728	0.7176	0.8471
SCA2	75	0.72	36.85	11.69	49.81	13.29	13.46	8.24	16.82	7.46	1.0367	0.0445	0.7882	0.8878
SCA3	138	0.93	39.25	11.81	50.34	12.04	10.92	7.32	14.98	8.78	1.1394	0.0402	0.7490	0.8654
SCA6	72	0.85	52.18	10.34	63.94	10.71	11.76	10.35	14.13	7.64	0.8575	0.0472	0.6980	0.8354
All	345	0.84	41.66	12.66	52.92	13.40	11.30	8.28	15.07	8.23	1.0471	0.0241	0.7344	0.8570

ISSN: 1750-1172