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Table 1 Summary of literature on the treatment of hip dysplasia in transplanted MPS I-H patients

From: Treatment of hip dysplasia in patients with mucopolysaccharidosis type I after hematopoietic stem cell transplantation: results of an international consensus procedure

First author (year of publication) Patients with hip dysplasia (total patients reported) Surgical interventions (n/o patients) Mean age at surgery (years) Mean follow-up after surgery (years) Radiological outcome Functional outcome
Field (1994) 11 (11) Femoral osteotomy (?) - - No acetabular remodeling -
Souillet (2003) 11 (15) Acetabular and femoral osteotomy (1) 7.4 1.4 No dislocation -
Femoral osteotomy (7)
Total hip replacement (1)
Weisstein (2004) 6 (7) Acetabular and femoral osteotomy (4) 4.8 - Mean acetabular angle from 38° to 20° Normal range of motion in 4/6
Pelvic osteotomy (2) Appropriate femoral head coverage
Taylor (2008) 23 (23) Acetabular and femoral osteotomy (8) 4.4 8.0 Mean acetabular angle from 34° to 22° Good range of motion
Acetabular osteotomy (4) Mean center edge-angle 40° (long term) Number of older patients complaining of hip discomfort
   Femoral osteotomy (1)