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Table 1 Summary of literature on the treatment of hip dysplasia in transplanted MPS I-H patients

From: Treatment of hip dysplasia in patients with mucopolysaccharidosis type I after hematopoietic stem cell transplantation: results of an international consensus procedure

First author (year of publication)

Patients with hip dysplasia (total patients reported)

Surgical interventions (n/o patients)

Mean age at surgery (years)

Mean follow-up after surgery (years)

Radiological outcome

Functional outcome

Field (1994)

11 (11)

Femoral osteotomy (?)

-

-

No acetabular remodeling

-

Souillet (2003)

11 (15)

Acetabular and femoral osteotomy (1)

7.4

1.4

No dislocation

-

Femoral osteotomy (7)

Total hip replacement (1)

Weisstein (2004)

6 (7)

Acetabular and femoral osteotomy (4)

4.8

-

Mean acetabular angle from 38° to 20°

Normal range of motion in 4/6

Pelvic osteotomy (2)

Appropriate femoral head coverage

Taylor (2008)

23 (23)

Acetabular and femoral osteotomy (8)

4.4

8.0

Mean acetabular angle from 34° to 22°

Good range of motion

Acetabular osteotomy (4)

Mean center edge-angle 40° (long term)

Number of older patients complaining of hip discomfort

  

Femoral osteotomy (1)

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