Figure 1

Sequential X-ray studies of a MPS I-H patient who underwent successful HSCT at the age of 2 yrs and 6 m as well as spinal fusion at the age of 7. Characteristic signs included acetabular dysplasia with a steep acetabular angle, interruption of Shenton’s line, characteristic medial thinning of the femoral head and coxa valga. A: at diagnosis, age 1 yrs 3 m B: at 2 yrs 4 m C: at 4 yrs 8 m D: at 8 yrs 5 m.