Figure 5

Typical audiograms for Stickler syndrome in general, and for STL3 and STL4. A) ARTA for Stickler patients in general (without genetic subclassification), based on the detailed audiometric results in 44 patients[14]. Mean air conduction thresholds of both ears are shown. B) ARTA for type III Stickler syndrome, based on the detailed audiometric results in 18 STL3 patients (52 different measurements)[17, 53]. Air conduction thresholds of the best ear are shown, unless in patients where an air-bone gap was present, in which bone conduction of the best ear is shown. C) Average audiogram for type IV Stickler syndrome, based on the detailed audiometric results in 7 STL4 patients (median age 15y)[8, 41]. Air conduction thresholds of the best ear are shown.