| Group 1 (N=21) | % | Group 2 (N=21) | % | Group 3 (N=28) | % | Total (N=73) | % |
---|---|---|---|---|---|---|---|---|
Bulbar palsy (CN IX-XII) | 18 | 86% | 21 | 100% | 25 | 89% | 67 | 92% |
Hearing loss | 14 | 67% | 19 | 90% | 24 | 86% | 59 | 81% |
Facial weakness | 10 | 48% | 20 | 95% | 23 | 82% | 56 | 77% |
Respiratory compromise | 18 | 86% | 13 | 62% | 13 | 46% | 47 | 64% |
Muscle weakness | 14 | 67% | 10 | 48% | 14 | 50% | 40 | 55% |
Upper motor neuron signs | 3 | 14% | 10 | 48% | 11 | 39% | 26 | 36% |
Palsy of CN III, IV or VI | 9 | 43% | 5 | 24% | 7 | 25% | 23 | 32% |
Stridor | 10 | 48% | 3 | 14% | 4 | 14% | 18 | 25% |
Palsy of the trigeminal nerve (V) | 1 | 5% | 6 | 29% | 6 | 21% | 14 | 19% |
Lower motor neuron signs | 4 | 19% | 5 | 24% | 4 | 14% | 13 | 18% |
Diaphragm weakness/palsy | 4 | 19% | 3 | 14% | 4 | 14% | 11 | 15% |
Palsy of the optic nerve (II) | 2 | 10% | 3 | 14% | 5 | 18% | 10 | 14% |
Ataxia | 2 | 10% | 3 | 14% | 3 | 11% | 9 | 12% |
Tremor | 2 | 10% | 1 | 5% | 3 | 11% | 6 | 8% |
Behavioral changes | 1 | 5% | 0 | 0% | 2 | 7% | 3 | 4% |
Mental retardation | 0 | 0% | 0 | 0% | 3 | 11% | 3 | 4% |
Epilepsy | 0 | 0% | 0 | 0% | 2 | 7% | 3 | 4% |
Autonomic dysfunction | 0 | 0% | 0 | 0% | 2 | 7% | 2 | 3% |