Internal neurofibromas | Odds ratio (95% CI)† | P value‡ | ||
---|---|---|---|---|
No | Yes | |||
n = 322 | n = 35 | |||
Male gender | 148 (46) | 16 (46) | 1.01 (0.49-2.07) | 0.977 |
Age (years) | 7.35 ± 4.87 | 10.67 ± 4.81 | 1.14 a (1.07-1.23) | <10 -4 |
Familial cases | 166 (51) | 17 (49) | 0.61 (0.29-1.27) | 0.184 |
Subcutaneous neurofibromas (n = 305/35) | 53 (17) | 19 (54) | 4.51 (2.13-9.55) | <10 -4 |
Cutaneous neurofibromas | 139 (43) | 14 (40) | 0.78 (0.37-1.64) | 0.512 |
Plexiform neurofibromas (n = 140/33) | 60 (43) | 19 (70) | 3.60 (1.55-8.34) | 0.003 |
Café-au-lait spots | 319 (99) | 35 (100) | 0.81 (0.04 - ∞) | 1.000 |
Freckles (n = 312/34) | 194 (56) | 13 (28) | 1.09 (0.47-2.52) | 0.840 |
Lisch nodules (n = 250/23) | 151 (60) | 9 (39) | 0.35 (0.14–0.86) | 0.05 |
Xanthogranulomas (n = 257/32) | 10 (4) | 4 (13) | 6.60 (1.69-25.74) | 0.007 |
Short stature (n = 293/32) | 32 (11) | 4 (13) | 1.00 (0.32-3.13) | 0.996 |
Macrocephaly (n = 302/34) | 12 (35) | 73 (24) | 1.65 (0.76-3.54) | 0.203 |
Nonunion | 1 (3) | 12 (4) | 1.8 (0.3-10.2) | 0.684 |
Dysplasia (=314/35) | 27 (9) | 4 (11) | 1.06 (0.34-3.35) | 0.914 |
Facial asymmetry (n = 261/24) | 20 (8) | 3 (12) | 1.23 (0.45-6.93) | 0.419 |
Hypertension (n = 298/31) | 2 (1) | 1 (3) | 5.41 (0.40-73.93) | 0.205 |