Patient number | Sex | Age at diagnosis (years) | Follow up (years) | BAL lymphocytes (%) | Organs involved (biopsied organ) |
---|---|---|---|---|---|
1* | M | 6.5 | 9.4 | 42 | Lung, lymphadenopathy |
2 | M | 8.0 | 3.6 | 48 | Lung, lymphadenopathy, eye (uveitis) |
3 | F | 13.8 | 2 | 64 | Lung, liver |
4 | M | 13.5 | 3.8 | 69 | Lung, lymphadenopathy, liver |
5 | M | 12.7 | 4.2 | 28 | Lung, lymphadenopathy |
6 | F | 8.2 | 2.7 | 49 | Lung, lymphadenopathy, bone marrow, spleen |
7 | F | 7.1 | 2.4 | 30 | Lung, lymphadenopathy, bowel |
8 | F | 11.2 | 4 | MD | Lung, skin |
9 | M | 14.4 | 3.1 | 20 | Lung, lymphadenopathy, parotid, eye, joints |
10 | M | 5.9 | 6.7 | 29 | Lung, skin, spleen |
11* | F | 9.1 | 9.1 | 59 | Lung, lymphadenopathy, liver, eye |
12 | F | 13 | 3.3 | MD | Lung, eye, liver, kidney, skin |
13 | F | 11.5 | 2.6 | 72 | Lung, joints, lymphadenopathy |
14 | F | 10.8 | 2 | 12 | Lung |
15 | M | 12.8 | 2.5 | 18 | Lung, liver, skin, eye, bone marrow |
16 | M | 5.6 | 5.2 | MD | Lung, larynx, tonsils |
17 | F | 14 | 4 | MD | Lung, joints, eye |
18 | F | 9.6 | 0.8 | 23 | Lung, liver, lymphadenopathy |
19 | F | 8.3 | 0.4 | MD | Lung |
20 | M | 9 | 9.2 | 50 | Lung |
21 | M | 9.3 | MD | MD | Lung, lymphadenopathy, central nervous system |
Total | Sex ratio 1 | Median 9.4 | Median 3.4 | Restricted to the lung = 3, multi-organic = 18 |