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Table 2 Aetiologic spectrum of interstitial lung disease (ILD) in children

From: A national internet-linked based database for pediatric interstitial lung diseases: the French network

Diagnoses Patients (n=) Patients (%) Sex ratio M/F Median age at diagnosis (years) Range
Surfactant disorders 36 17.6 1.0 0.3 (0–12.3)
Haemosiderosis 23 11.2 0.3 4.8 (0.7-14)
Granulomatous diseases (sarcoidosis) 21 10.2 1.0 9.6 (5.6-14.4)
Alveolar proteinosis 20 9.7 1.8 0.6 (0–13.6)
Exposure diseases 9 4.4 0.8 10.6 (2.2-14.4)
Connective disorders and vascularitis 9 4.4 0.6 12.4 (0.1-15.7)
Metabolic disorders 5 2.4 0.7 1.7 (0–4)
Langerhans' cell histiocytosis 5 2.4 1.5 1.1 (0.5-7.3)
Infectious diseases 4 2.0 1.0 0.2 (0–6.6)
Eosinophilic lung diseases 4 2.0 1.0 10.0 (5.1-16.9)
Lymphatic disorders 4 2.0 0.3 0 (0–14.5)
Others 9 4.4 2.0 1.3 (0–12.8)
Undiagnosed 56 27.3 1.0 0.7 (0–16.4)
Total 205 100 0.9 1.5 (0–16.9)
  1. Abbreviations: M: male; F: female.