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Table 2 Aetiologic spectrum of interstitial lung disease (ILD) in children

From: A national internet-linked based database for pediatric interstitial lung diseases: the French network

Diagnoses

Patients (n=)

Patients (%)

Sex ratio M/F

Median age at diagnosis (years)

Range

Surfactant disorders

36

17.6

1.0

0.3

(0–12.3)

Haemosiderosis

23

11.2

0.3

4.8

(0.7-14)

Granulomatous diseases (sarcoidosis)

21

10.2

1.0

9.6

(5.6-14.4)

Alveolar proteinosis

20

9.7

1.8

0.6

(0–13.6)

Exposure diseases

9

4.4

0.8

10.6

(2.2-14.4)

Connective disorders and vascularitis

9

4.4

0.6

12.4

(0.1-15.7)

Metabolic disorders

5

2.4

0.7

1.7

(0–4)

Langerhans' cell histiocytosis

5

2.4

1.5

1.1

(0.5-7.3)

Infectious diseases

4

2.0

1.0

0.2

(0–6.6)

Eosinophilic lung diseases

4

2.0

1.0

10.0

(5.1-16.9)

Lymphatic disorders

4

2.0

0.3

0

(0–14.5)

Others

9

4.4

2.0

1.3

(0–12.8)

Undiagnosed

56

27.3

1.0

0.7

(0–16.4)

Total

205

100

0.9

1.5

(0–16.9)

  1. Abbreviations: M: male; F: female.