Diagnoses
|
Patients (n=)
|
Patients (%)
|
Sex ratio M/F
|
Median age at diagnosis (years)
|
Range
|
---|
Surfactant disorders
|
36
|
17.6
|
1.0
|
0.3
|
(0–12.3)
|
Haemosiderosis
|
23
|
11.2
|
0.3
|
4.8
|
(0.7-14)
|
Granulomatous diseases (sarcoidosis)
|
21
|
10.2
|
1.0
|
9.6
|
(5.6-14.4)
|
Alveolar proteinosis
|
20
|
9.7
|
1.8
|
0.6
|
(0–13.6)
|
Exposure diseases
|
9
|
4.4
|
0.8
|
10.6
|
(2.2-14.4)
|
Connective disorders and vascularitis
|
9
|
4.4
|
0.6
|
12.4
|
(0.1-15.7)
|
Metabolic disorders
|
5
|
2.4
|
0.7
|
1.7
|
(0–4)
|
Langerhans' cell histiocytosis
|
5
|
2.4
|
1.5
|
1.1
|
(0.5-7.3)
|
Infectious diseases
|
4
|
2.0
|
1.0
|
0.2
|
(0–6.6)
|
Eosinophilic lung diseases
|
4
|
2.0
|
1.0
|
10.0
|
(5.1-16.9)
|
Lymphatic disorders
|
4
|
2.0
|
0.3
|
0
|
(0–14.5)
|
Others
|
9
|
4.4
|
2.0
|
1.3
|
(0–12.8)
|
Undiagnosed
|
56
|
27.3
|
1.0
|
0.7
|
(0–16.4)
|
Total
|
205
|
100
|
0.9
|
1.5
|
(0–16.9)
|
- Abbreviations: M: male; F: female.