Diagnoses | Patients (n=) | Patients (%) | Sex ratio M/F | Median age at diagnosis (years) | Range |
---|---|---|---|---|---|
Surfactant disorders | 36 | 17.6 | 1.0 | 0.3 | (0–12.3) |
Haemosiderosis | 23 | 11.2 | 0.3 | 4.8 | (0.7-14) |
Granulomatous diseases (sarcoidosis) | 21 | 10.2 | 1.0 | 9.6 | (5.6-14.4) |
Alveolar proteinosis | 20 | 9.7 | 1.8 | 0.6 | (0–13.6) |
Exposure diseases | 9 | 4.4 | 0.8 | 10.6 | (2.2-14.4) |
Connective disorders and vascularitis | 9 | 4.4 | 0.6 | 12.4 | (0.1-15.7) |
Metabolic disorders | 5 | 2.4 | 0.7 | 1.7 | (0–4) |
Langerhans' cell histiocytosis | 5 | 2.4 | 1.5 | 1.1 | (0.5-7.3) |
Infectious diseases | 4 | 2.0 | 1.0 | 0.2 | (0–6.6) |
Eosinophilic lung diseases | 4 | 2.0 | 1.0 | 10.0 | (5.1-16.9) |
Lymphatic disorders | 4 | 2.0 | 0.3 | 0 | (0–14.5) |
Others | 9 | 4.4 | 2.0 | 1.3 | (0–12.8) |
Undiagnosed | 56 | 27.3 | 1.0 | 0.7 | (0–16.4) |
Total | 205 | 100 | 0.9 | 1.5 | (0–16.9) |