From: Delineation and Diagnostic Criteria of Oral-Facial-Digital Syndrome Type VI
Molar tooth sign (MTS)* and one or more of | 1. Tongue hamartoma(s) and/or additional frenula and/or upper lip notch |
 | 2. Mesoaxial polydactyly of one or more hands or feet |
 | 3. Hypothalamic hamartoma |