DEMOGRAPHIC AND CLINICAL DATA | ||||
---|---|---|---|---|
SEX | Â | Â | Â | Â |
 | Total | Males | Females |  |
Nr (%) | 233 | 119 (49%) | 114 (51%) | Â |
Age at Interview, Mean ± SD (years) | 51.1 ± 16.9 | 52.4 ± 17.2 | 49.7 ± 16.6 | p = ns |
[Range] | [10;84] | [11;81] | [10;84] | |
EDUCATION LEVEL | Â | Â | Â | Â |
 | Low | Interm | High |  |
Nr (%) | 53 (23%) | 69 (30%) | 111 (47%) | Â |
Age at Interview, Mean ± SD (years) | 62.5 ± 16.9 | 49.9 ± 16.2 | 46.4 ± 14.9 | P < 0.0001 |
[Range] | [10;84] | [15;78] | [16;75] | |
AFFECTED GENE | Â | Â | Â | Â |
 | HHT1 | HHT2 | HHT? |  |
Nr (%) | 81 (35%) | 132 (56%) | 20 (9%) | Â |
Age at Interview, Mean ± SD (years) | 46.6 ± 16.9 | 52.4 ± 16.8 | 60.1 ± 13.3 | P < 0.003 |
[Range] | [11;79] | [10;84] | [36;80] | |
INDEX/NON-INDEX STATUS | Â | Â | Â | Â |
 | Index | Non-Index |  |  |
Nr (%) | 112 (48.1%) | 121 (51.9%) | Â | Â |
Age at Interview, Mean ± SD (years) | 57.4 ± 14.1 | 45.2 ± 17.3] |  | P < 0.0001 |
[Range] | [15;81] | [10;84] | Â | |
CLINICAL DATA | Nr (%) | Â | Â | |
Epistaxis | 231 (99.1%) | Â | Â | |
Mucocutaneous Telangiectases | 233 (100%) | Â | Â | |
PAVM | 117 (50.2%) | Â | Â | |
CAVMs | 19 (8.1%) | Â | Â | |
HAVMs | 182 (78.1%) | Â | Â | |
GI bleeding | 62 (26.6%) | Â | Â |