Figure 5From: Copper and bezafibrate cooperate to rescue cytochrome c oxidase deficiency in cells of patients with sco2 mutationsCOX activity in fibroblasts of a second SCO2 patient and of a SURF1 patient were treated with 400 μM BZF for five days. In SCO2 patient 2 the analysis could be performed only in duplicate in BZF-treated cells. * = significant versus untreated (p<0.05).Back to article page