Table 1 Comparison of type 1 and type 2 autoimmune pancreatitis (AIP).
| Â | Type 1AIP | Type 2 AIP |
|---|---|---|
Age | Adult | Child and adult |
Gender | Predominantly male | Almost equal |
Serum IgG4 levels | Elevated | Normal |
Histology | Â | Â |
   Histological nomenclature | Lymphoplasmacytic sclerosing pancreatitis (LPSP) | Idiopathic duct-centric pancreatitis |
   IgG4+ plasma cells | Many | Rare |
   Granulocytic epithelial lesion | Absent | Present |
Relapse rate | High | Low |
Extra-pancreatic lesions | IgG4-related disease as shown in Table 2 | Inflammatory bowel disease |