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Table 3 Distribution of the IPCCC codes in the ten categories of the anatomic and clinical classification of congenital heart defects (ACC-CHD) in the EPICARD study

From: Population-based evaluation of a suggested anatomic and clinical classification of congenital heart defects based on the International Paediatric and Congenital Cardiac Code

Group

Number of codes

Number of CHD cases

%

1. Heterotaxy, including isomerism and mirror-imagery

1

2

3

4

5

6

1

3

7

10

14

2

37

2.7

8.1

18.9

27

37.9

5.4

100.0

2. Anomalies of the venous return

1

2

3

4

5

6

28

3

0

0

0

0

31

90.3

9.7

0.0

0.0

0.0

0.0

100.0

3. Anomalies of the atria and interatrial communications

1

2

3

4

5

6

159

19

4

0

0

0

182

87.4

10.4

2.2

0.0

0.0

0.0

100.0

4. Anomalies of the atrioventricular junctions and valves

1

2

3

4

5

6

158

44

9

1

1

0

213

74.2

20.6

4.2

0.5

0.5

0.0

100.0

5. Complex anomalies of atrioventricular connections

1

2

3

4

5

6

5

3

4

0

1

0

13

38.5

23.1

30.8

0.0

7.7

0.0

100.0

6. Functionally univentricular hearts

1

2

3

4

5

6

100

34

15

3

6

0

158

63.3

21.5

9.5

1.9

3.8

0.0

100.0

7. Ventricular septal defects (VSD)

1

2

3

4

5

6

1337

135

19

1

0

0

1492

89.6

9

1.3

0.1

0.0

0

100.0

8. Anomalies of the ventricular outflow tracts (ventriculo-arterial connections)

1

2

3

4

5

6

404

96

43

17

3

0

563

71.8

17.1

7.6

3.0

0.5

0.0

100.0

9. Anomalies of the extrapericardial arterial trunks

1

2

3

4

5

6

78

68

16

5

2

0

169

46.1

40.2

9.5

3

1.2

0.0

100.0

10. Congenital anomalies of the coronary arteries

1

2

3

4

5

6

9

0

0

0

0

0

9

100.0

0.0

0.0

0.0

0.0

0.0

100.0