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Table 2 Plasma lipid, apolipoprotein, and lipoprotein analysis in two AD subjects after a fat load*.

From: Molecular analysis and intestinal expression of SAR1 genes and proteins in Anderson's disease (Chylomicron retention disease)

Patients

AD1

AD3

Fasting normal range

After a fat load, T90-T180

 

T0

T90

T180

T0

T90

T180

  

Total cholesterol

1.06

1.03

1.09

0.90

0.91

0.94

1.20-2.20

No change

LDL-cholesterol

0.73

0.70

0.76

0.56

0.56

0.62

0.40-1.10

 

HDL-cholesterol

0.21

0.22

0.21

0.19

0.20

0.19

0.40-0.65

 

Triglycerides

0.58

0.57

0.58

0.74

0.74

0.66

0.35-1.30

1.68-2.04

ApoA-I

0.71

0.68

0.67

0.65

0.63

0.59

1.30-1.80

 

ApoB

0.68

0.65

0.65

0.57

0.58

0.53

0.50-1.00

 

Chylomicrons in serum

Absent

Absent

Absent

Absent

Absent

Absent

Absent

Present

Presence of apoB48 in isolated lipoproteins

No

No

No

No

No

No

No

Yes

Presence of apoB100 in isolated lipoproteins

Yes

Yes

Yes

Yes

Yes

Yes

Yes

Yes

  1. *Values are given in g/L.