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Table 1 Diagnostic criteria for Neurofibromatosis type 2 (these include the NIH criteria with additional criteria)

From: Neurofibromatosis type 2 (NF2): A clinical and molecular review

Main criteria Additional criteria
Bilateral vestibular schwannomas (VS) or family history of NF2 plus Unilateral VS plus any two of: meningioma, glioma, neurofibroma, schwannoma, and posterior subcapsular opacities
1) Unilateral VS or or
2) Any two of: meningioma, glioma, neurofibroma, schwannoma, posterior subcapsular lenticular opacities Multiple meningioma (two or more) plus unilateral VS or any two of: glioma, neurofibroma, schwannoma, and cataract
  1. NF2 – Neurofibromatosis type 2; NIH – National Institutes of Health; VS – vestibular schwannomas