| FVC > 75% | FVC < 75% | p-value between groups 2–3 | |
---|---|---|---|---|
 | Group 1 | Group 2 (NPPV) | Group3 (not vent) |  |
N | 44 | 16 | 12 | Â |
male/female | 27/17 | 9/7 | 7/5 | Â |
Age | 51.16 (7.39) | 55.93 (5.09) | 57.54 (6.54) | ns |
BMI | 22.72 (3.90) | 21.98 (4.48) | 22.85 (3.16) | ns |
Bulbar onset | 13/44 | 5/16 | 4/12 | ns |
Spinal onset | 23/44 | 8/16 | 6/12 | ns |
FVC% | 83.3 (11.84) | 65.13 (13.37) | 62.35 (12.75) | ns |
FEV1% | 88.12 (13.98) | 64.53 (14.17) | 61.6 (13.8) | ns |
PaO2 mmHg | 90.35 (9.58) | 79.91 (12.48) | 77.35 (8.54) | ns |
PaCO2 mmHg | 36.43 (6.72) | 41.83 (9.27) | 39.48 (8.92) | ns |
ALSFRS-R | Â | 28.7 (6.1) | 26.7 (7.1) | ns |