Table 2 Median and mean survival of MPS I patients
SURVIVAL (years) | ||
|---|---|---|
median (approximate 95% CI) | mean (approximate 95% CI) | |
MPS I (ALL) | 11.6 (9.5 to 13.7) | 14.6 (13.0 to16.1) |
HURLER (ALL) | 8.7 (7.6 to 9.7) | 10.5 (8.8 to12.2) |
HURLER with censoring for BMT | 6.8 (5.6 to 8.0) | 6.6 (5.7 to 8.4) |
HURLER that received BMT | Can not estimate | 15.6 (12.5 to 18.8) |
HURLER that did not receive BMT | 8.0 (7.0 to 8.9) | 7.9 (7.0 to 8.8) |
HURLER post-BMT survival | Can not estimate | 14.4 (11.5 to 17.4) |
HURLER-SCHEIE | Can not estimate | 21.6 (19.3 to 24.0) |
SCHEIE | Can not estimate | Can not estimate (1 death only) |