Study Region | Ascertainment period | No. of cases | No. of live births | Syndrome subtype | Birth Prevalence/100,000 |
---|---|---|---|---|---|
Lowry (1971) [8]British Columbia | 1952 – 1968 | 7 | 606,157 | All | 1.15 |
Hurler | 0.99 | ||||
Scheie | 0.16 | ||||
Lowry (1990) [9]British Columbia | 1952 – 1986 | 7 | 665,702 | All | 0.77 |
Hurler | 0.69 | ||||
Scheie | 0.08 | ||||
Nelson (1997) [10]N. Ireland | 1958 – 1985 | 14 | 839,520 | All | 1.66 |
Hurler | 1.30 | ||||
Hurler-Scheie | 0.36 | ||||
Scheie | No cases | ||||
Nelson (2003) [11]Western Australia | 1969 – 1996 | 6 | 641,178 | All | 0.93 |
Hurler | 0.93 | ||||
Hurler-Scheie | No cases | ||||
Scheie | No cases | ||||
Poorthuis (1999) [12]Netherlands | 1970 – 1996 | 82 | 6,871,909 | All | 1.19 |
Meikle (1999) [13]Australia | 1980 – 1996 | 38† | 3,344,000 | All | 1.14 |
Hutchesson (1998) [14]West Midlands UK | 1981 – 1991 | 7 | 707,720 | All | 0.99 |
Baehner (2005) [15]Germany | 1980 – 1995 | 93 | 13,410,924 | All | 0.69 |
Hurler | 0.61 | ||||
Hurler-Scheie | 0.03 | ||||
Scheie | 0.05 | ||||
This Study England & Wales | 1981 – 2003 | 167 | 15,611,220 | All | 1.07 |
Hurler | 0.76 | ||||
Hurler-Scheie | 0.24 | ||||
Scheie | 0.07 |