LQTS subtypes | Gene | Prevalence (% of all genotyped cases) |
---|---|---|
LQT1 and JLN1 (AR) | KCNQ1 | >50 |
LQT2 | KCNH2 | 35–40 |
LQT3 | SCN5A | 10–15 |
LQT4 | ANK2 | Â |
LQT5 (RWS) and JLN2 | KCNE1 | Â |
LQT6 | KCNE2 | Â |
LQT7 (Andersen-Tawil syndrome)* | KCNJ2 | Â |
LQT8 (Timothy syndrome) | CACNA1c | Â |
LQT9 | CAV3 | Â |
LQT10 | SCN4B | Â |