Figure 2

5-year-old patient affected by LQTS with congenital deafness. Tracing recorded during a syncopal episode. T wave alternans precedes the onset of torsade de pointes. In this case, it is also evident that TdP is not preceded by a pause. (From C. Pernot: Le syndrome cardio-auditif de Jervell et Lange-Nielsen. Aspects electrocardiographiques. Proc Ass Europ Paediat Cardiol 1972, 8:28–36).