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Figure 2 | Orphanet Journal of Rare Diseases

Figure 2

From: Hypoxanthine-guanine phosophoribosyltransferase (HPRT) deficiency: Lesch-Nyhan syndrome

Figure 2

Management of self-injurious behaviour. The cornerstone of day-to-day management of Lesch-Nyhan syndrome is still adapted physical restraint to protect patients from themselves. For instance, elbow restraints allow hand use without the possibility of finger mutilation, and dental guards prevent cheek biting. Patients themselves request restrictions and became anxious if they are unrestrained.

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