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Table 7 Conditions for which the validity of their association in Sweet's syndrome patients remains to be established

From: Sweet's syndrome – a comprehensive review of an acute febrile neutrophilic dermatosis

Alpha 1-antitrypsin deficiency [42]

Anti-factor VIII inhibitor [287]

Antiphospholipid syndrome [1]

Aortitis (Takayasu's arteritis) [286,288]

Aplastic anemia [39,99]

Autoimmune disorders: autoimmune thrombocytopenic purpura [401], connective tissue disease (undifferentiated) [401], dermatomyositis [20], lupus erythematosus (subacute [289] and systemic [119,290,401]), pemphigus vulgaris [291] and Sjogren's syndrome [12,17,265,433]

Bronchiolitis obliterans and organizing pneumonia [292-294]

Chemical fertilizer [158]

Chronic fatigue syndrome [295]

Cirrhosis (cryptogenic) [30]

Cholelithiasis [421]

Common bile duct and intrahepatic duct stones [19]

Congenital dyserythropoietic anemia [18]

Congenital neutropenia (Kostmann's syndrome) [97]

Cutis laxa (acquired, Marshall syndrome) [38,42,245,246]

Dressler's syndrome (postmyocardial infarction syndrome) [17]

Eosinophilic granuloma [19]

Fanconi anemia [36,241]

Glycogen storage disease (Type Ib) [41]

Granuloma annulare [296]

IgA nephropathy (Berger's disease) [97]

Immunizing agent (BCG vaccination and flu) [17,297,298,419]

Immunodeficiency diseases: chronic granulomatous disease [37,299,300], complement deficiency [30], human immunodeficiency virus infection [98,254,302], and primary T-cell immunodeficiency disease [43,303])

Infections: Anaplasma phagocytophilum [304], bartholinitis [17], bronchitis [17], Capnocytophaga canimorsus [305], chlamydia [306-308], cholangitis [19], cholecystitis [12], coccidioidomycosis [309], cytomegalovirus [1,310,311], Entamoeba histolytica [214], Epstein-Barr virus [1], Francisella tularensis [312], Helicobacter pylori [313], hepatitis (acute hepatitis B [314], autoimmune [251], cholestatic [30], chronic active [315], hepatitis C [161], and prior hepatitis A [1]), herpes simplex [316,317], herpes zoster [119], histoplasmosis [259], human immunodeficiency virus [98,254,302], leprosy [19], lymphadenitis (not otherwise specified [318,319] and subacute necrotizing [212,318]), mycobacteria (nontuberculous) [19,212,316,320-322,401], otitis media [12,17], pancreatitis [30], Pasteurella multocida bronchitis [323], Penicillium species [401], Pneumocystis carinii pneumonia [324], pyelonephritis [12], Salmonella (group D cervical lymphadenitis) [401], Staphylococcus aureus [44,326,431], Staphylococcus epidermidis (methicillin resistant) [407], subacute bacterial endocarditis [327], tonsillitis [12,17,19], toxoplasmosis [328], Trichophyton rubrum [418], tuberculosis [17,329,330], ureaplasmosis [331], urinary tract [17,20], and vulvovaginitis [12,20]

Malabsorption [30]

Mid-dermal elastolysis [332]

POEMS syndrome (polyneuropathy, organomegaly, endocrinopathy, M protein, and skin changes) [333]

Postoperative (pneumonectomy) [334]

Psoriasis vulgaris [16]

Rhinosinusitis [335]

SAPHO syndrome (synovitis, acne, pustulosis, hyperostosis, and osteomyelitis) [424]

Still's disease [336]

Thermal injury [160]

Transient acantholytic dermatosis (Grover's disease) [337]

Ureter obstruction [338]

Urticaria (chronic) [17]

Urticaria pigmentosa [12]

Welding burns [339]

  1. Source [1]: Adapted with permission from Cohen PR, Kurzrock R: Sweet's syndrome revisited: a review of disease concepts. Int J Dermatol 2003;42:761–778. Copyright 2003, Reprinted with permission from the International Society of Dermatology, Blackwell Publishing Ltd, Oxford, United Kingdom.