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Table 6 Distribution of diagnoses in the HP Study [4]

From: Hypersensitivity pneumonitis

Diagnosis

Number of patients

Hypersensitivity pneumonitis

199

Pigeon breeder's/bird fancier's disease

132

Farmer's lung

38

Humidifier lung

3

Suberosis

2

Summer type HP

2

Various exposures to fungi

19

HP of unknown origin

3

Controls

462

Idiopathic interstitial pneumonia *

226

Sarcoidosis

52

Interstitial disease associated with collagen vascular disease

35

Drug induced pulmonary disease

26

Bronchiolitis obliterans (with our without organizing pneumonia)

25

Unspecified interstitial lung disease †

26

Infectious pneumonia

11

Histiocytosis X

10

Asthma

6

Silicosis

5

Eosinophilic pneumonia

5

Normal lung

4

Bronchoalveolar carcinoma/carcinomatous lymphangitis

4

Residual HP ‡

3

Residual HP ‡

3

Organic dust toxic syndrome

3

Lymphocytic interstitial pneumonia

2

Pulmonary edema (heart failure)

2

Radiation pneumonitis

2

Miscellaneous §

13

TOTAL

661

  1. * includes patients with the clinical diagnosis of idiopathic pulmonary fibrosis, and those with the pathological diagnoses of usual, desquamative, respiratory bronchiolitis, acute and non-specific interstitial pneumonia;
  2. † includes patients in whom no specific diagnosis could be reached but in whom HP was excluded on the basis of BAL;
  3. ‡ includes late emphysematous or fibrotic sequelae of HP in which the typical alveolar lymphocytosis of active HP has disappeared;
  4. §includes single cases of alveolar hemorrhage, anthracosis, berylliosis, Churg-Strauss syndrome, diffuse panbronchiolitis, hepato-pulmonary syndrome, HIV-associated nonspecific interstitial pneumonia, necrotizing sarcoid granulomatosis, pulmonary amyloidosis, alveolar proteinosis, crack lung, Pneumocystis carinii pneumonia, and Wegener's granulomatosis.