From: Thalassemias in South Asia: clinical lessons learnt from Bangladesh
Diseases types | n (%) | Median age (year) at diagnosis | Transfusion status #/n (%) | ||
---|---|---|---|---|---|
TDT | NTDT | Not required | |||
Hb-E-beta thalassemia | 910 (77.25) | 3.5 | 522/840 (62.14) | 238/840 (28.33) | 80/840 (9.52) |
Beta thalassemia major | 173 (14.69) | 0.58 | 172/173 (99.42) | 1/173 (0.58) | 0/173 (0) |
Beta thalassemia trait | 64 (5.43) | 27.5 | 8/26 (30.77) | 14/26 (53.85) | 4/26 (15.38) |
Hb E disease | 12 (1.02) | 9 | 3/11 (27.27) | 3/11 (27.27) | 5/11 (45.45) |
Hb-E trait | 14 (1.19) | 26 | 2/8 (25) | 3/8 (37.50) | 3/8 (37.50) |
Others (H, Punjab D etc.) | 5 (0.42) | 4 | 5/5 (100) | 0/5 (0) | 0/5 (0) |
Total | 1178 | Â | 712/1063 (66.98) | 259/1063 (24.36) | 72/1063 (8.66) |