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Table 1 Pattern of thalassemia and transfusion practice in Bangladesh

From: Thalassemias in South Asia: clinical lessons learnt from Bangladesh

Diseases types

n (%)

Median age (year) at diagnosis

Transfusion status #/n (%)

TDT

NTDT

Not required

Hb-E-beta thalassemia

910 (77.25)

3.5

522/840 (62.14)

238/840 (28.33)

80/840 (9.52)

Beta thalassemia major

173 (14.69)

0.58

172/173 (99.42)

1/173 (0.58)

0/173 (0)

Beta thalassemia trait

64 (5.43)

27.5

8/26 (30.77)

14/26 (53.85)

4/26 (15.38)

Hb E disease

12 (1.02)

9

3/11 (27.27)

3/11 (27.27)

5/11 (45.45)

Hb-E trait

14 (1.19)

26

2/8 (25)

3/8 (37.50)

3/8 (37.50)

Others (H, Punjab D etc.)

5 (0.42)

4

5/5 (100)

0/5 (0)

0/5 (0)

Total

1178

 

712/1063 (66.98)

259/1063 (24.36)

72/1063 (8.66)

  1. NTDT, non-transfusion dependent thalassemia; TDT, transfusion dependent thalassemia