From: Cardiac pathology in spinal muscular atrophy: a systematic review
Arrhythmias in patients with SMA type 3 | ||
---|---|---|
Arrhythmia type | Anatomical site of origin | Reported ECG abnormalities (number of times observed in patients with SMA type 3) |
Impulse initiation disorder | Sinus/SA node initiation disorders | Sinus arrest (2) |
Sinus dysfunction (1) | ||
Sinus tachycardia (1) | ||
Supraventricular initiation disorders | Atrial fibrillation (5) | |
AV junctional rhythm (5) | ||
Supraventricular extrasystoles (2) | ||
Atrial flutter (2) | ||
Atrial tachycardia (1) | ||
Ventricular initiation disorders | Ventricular extrasystoles (2) | |
Non-sustained ventricular tachycardias (2) | ||
Impulse conduction disorders | n/a | Left anterior hemiblock (4) |
AV-block (n.o.s.) (3) | ||
Right bundle branch block (3) | ||
1st degree AV block (3) | ||
Complete AV block (2) | ||
2nd degree AV block, Mobitz I (Wenckebach) (1) | ||
Prolonged junctional recovery time (1) |