Table 1 Clinical characteristics in 14 symptomatic children with hereditary angioedema

Age at onset (years)

Median 4 [1–11]

 Abdominal

6/14 (43%)

 Peripheral

8/14 (57%)

 Upper airway

0

 Abdominal

14/14 (100%)

 Peripheral

11/14 (79%)

 Upper airway

4/14 (29%)

Number of attacks within the observation period (45 months)^a

Median 13 [4–121]

 None

1/14 (7%)

 Rare (< one attack per month)

10/14 (72%)

 Frequent (≥ one attack per month)

3/14 (21%)