Manifestation | Maldonado et al. [6], N = 41 | Hoque et al. [5], N = 11 | Piraccini et al. [7], N = 21 | Nordkild et al. [8], N = 97 | Varney et al. [9], N = 17 | Pavlidakey et al. [10], N = 62 |
---|---|---|---|---|---|---|
Yellow nails, n (%) | 41 (100) | 10 (91) | 21 (100) | 86 (89) | 17 (100) | 53 (85) |
Chronic pulmonary manifestations, n (%) | 23 (56) | 7 (64) | 15 (71) | 61 (63) | 17 (100) | 24 (39) (PEs only) |
Lymphedema, n (%) | 26 (63) | 6 (55) | 6 (29) | 78 (80) | 13 (76) | 45 (72) |
Sinusitis, n (%) | 17 (41) | 3 (27) | 3 (14) | NR | 14 (83) | 11 (18) |
Complete triad | ~60% | 27% | 29% | NR | 76% | 27% |