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Table 3 Video-laryngoscopic examination results in patients with late-onset Pompe disease

From: Analysis of voice quality in patients with late-onset Pompe disease

ID

Larynx diagnosis

Age of dysphonia/duration

GRBAS

MPT

Vestibulum of larynx

Vocal folds

Arytenoid area

1

N

No

00000

6 s.

N

GI pp, VF thickened, thick mucus

Min. C

2

N

No

00000

8 s.

N

Min. VF thickened

N

3

GI Laryngeal tremor

No data

00100

10 s.

N

GI mp, VF tremor thick mucus on VF

C, O

4

N

No data

10100

4 s.

N

VFC, mucus on VF

N

5

Hyperfunctional dysphonia

No data

00001

10 s.

Phonation of VsP

N

C

6

No data

No data

No data

No data

No data

No data

No data

7

GI

4 H, silent soundless matte V

00220

12 s.

N

GI mp

Min. C, O

8

GI

13/0.1, silent soundless matte V

10110

12 s.

N

GI mp

C, O, mucus retention

9

N

No

00000

20 s.

N

N

N

10

GI Laryngitis posterior

25/10 H

10000

15 s.

N

GI

C, O Laryngitis posterior

11

N

No

00000

15 s

N

N

N

12

GI

30/8 morning H cough

00000

18 s.

N

GI mp

Min. C

13

No data

No data

No data

No data

No data

No data

No data

14

GI

37/10

00110

8 s.

Enlarged rVsF covers rVF

GI Oblique orientation of glottis.

N

15

GI

No V fatigue

00110

11 s.

N

GI mp. VF C

C, O

16

N

No

00100

5 s.

N

VF thickened, tremor

Min. C, O

17

GI

38/4

00100

22 s.

N

GI mp

C, O

18

GI

No V fatigue

10000

5 s.

N

GI mp

Min. C. As. r aryt. Moved forward

19

GI

No data

00100

4 s.

N

GI mp

N

  1. Table 3. GI - Glottal insufficiency; VF – vocal folds; VsF – vestibular folds; C – congestion; O - oedema; mp - middle part of the glottis; Min. – minimal; H – hoarseness; V – voice; r – right; N – normal, MPT –maximum phonation time