From: Urea cycle disorders in Spain: an observational, cross-sectional and multicentric study of 104 cases
Drug | Patients (N) | Mean ± SD (mg/kg/day) |
---|---|---|
Sodium phenylbutyrate | 50 | 250 ± 158 |
Sodium benzoate | 4 | 184 ± 92.3 |
Combined treatment | 10 | |
Sodium phenylbutyrate | 250 ± 134 | |
Sodium benzoate | 165 ± 80.5 | |
Carglumic acid | 1 | 15 |