Table 8 Diet treatment according to age group
From: Urea cycle disorders in Spain: an observational, cross-sectional and multicentric study of 104 cases
Age (N = 93) | 0-1y (N = 4) | 1-10y (N = 47) | 11-18y (N = 20) | >18y (N = 22) | |
|---|---|---|---|---|---|
Total proteins (g/kg/day) | 1.86 (0.90-2.95) | 0.95 (0.7-1.2) | 0.84 (0.65-0.94) | 0.7 (0.57-0.92) | |
Energy (calories) (kcal/kg/day) | 102 (92.5-140) | 72 (58-95) | 40 (32-43,5) | 36 (30-42) | |
Essential Aminoacids (g/kg/day) | 0.39 (0.2-0.5) | 0.3 (0.27-0.43) | 0.25 (0.14-0.48) | 0.2 (0.11-0.41) | |
Age | <6 m | 6-12 m | 1-10y | 11-16y | >16y |
WHO/FAO/UNU* (safe levels proteins) | 1.77 | 1.31 | 0.92-1.14 | 0.84-0.90 | 0.84-0.87 |
UK practice (N = 45)** Proteins | 2 (0.7-2.5) | 1.6 (1.2-1.8) | 1.3 (1-1.7) | 0.9 (0.7-1.4) | 0.8 (0.4-1.2) |