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Figure 4 | Orphanet Journal of Rare Diseases

Figure 4

From: Polycystic liver disease: an overview of pathogenesis, clinical manifestations and management

Figure 4

Indications and considerations for treatment strategies in symptomatic PLD. Schematic overview of relevant indications and considerations in PLD management. Patient characteristics and liver phenotype such as severity of clinical symptoms, age, (surgical) history, degree of hepatomegaly, and number, size and location of hepatic cysts are essential parameters for this decision. In general, the choice of procedure is an individual process in consultation with the patient. Severely affected individuals are patients with massive hepatomegaly, refractory symptoms, PLD-related complications and/or end-stage liver failure. Care and follow-up of these patients should be managed with caution. *Notification: Results about treatment efficacy of prolonged or long-term somatostatin analogue use is unknown. **Arbitrary total liver volume (TLV), because this outcome measurement is related to other parameters such as height, total body surface and sex. ***For example: recurrent hepatic cyst infection, HVOO.

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