From: Atypical hemolytic uremic syndrome
CFH mutation
CFI mutation
MCP mutation
C3 mutation
CFB mutation
THBD mutation
Anti -CFH Ab
None
Decreased C3 concentration
(< 2SD)
(% patients)
30-50%
20-30%
0-27%
70-80%
100%
50%
40-60%
up to 20%