From: Safety and caregiver satisfaction with gastrostomy in patients with Ataxia Telangiectasia
Pt. | Sex | Age GT Placed(yrs) | Years Post GT | BMI Z-Score1 | A-T Neurologic Score2 | Dysphagia3 | Immunologic Status | Reason(s) for GT | Alive at Time of Survey | Cause of Death | |
---|---|---|---|---|---|---|---|---|---|---|---|
 |  |  |  |  |  |  | IgA | IgG |  |  |  |
Patients tolerating GT placement | |||||||||||
1 | F | 10 | <1 | Â | Â | No | Normal | Deficient | Nutrition | Yes | Â |
2 | M | 15 | <1 | -1.76 | 35 | Yes: P | Deficient | Normal | Nutrition, GER treated w/nissen fundoplication | Yes | Â |
3 | M | 6 | 1 | 0.90 | Â | No | Normal | Deficient | Nutrition, GER, pulmonary infections | Yes | Â |
4 | F | 10 | 1 | -6.23 | 68 | No | Normal | Deficient | Nutrition | Yes | Â |
5 | M | 12 | 1 | -2.77 | 51 | No | Deficient | Normal | Nutrition | Yes | Â |
6 | F | 13 | 1 | Â | Â | Yes: P | Normal | Normal | Nutrition, dysphagia | Yes | Â |
7 | F | 15 | 1 | -0.44 | 40 | No | Deficient | Deficient | Nutrition | Yes | Â |
8 | M | 15 | 1 | -5.72 | 36 | No | Normal | Normal | Nutrition, dysphagia | Yes | Â |
9 | M | 10 | 2 | -8.17 | 59 | No | Deficient | Normal | Nutrition | Yes | Â |
10 | M | 10 | 3 | Â | Â | No | Deficient | Normal | Nutrition, cancer | Yes | Â |
11 | M | 13 | 3 | -0.65 | 38 | Yes: P | Deficient | Normal | Nutrition, LL pneumonia | Yes | Â |
12 | M | 10 | 4 | -4.25 | 32 | Yes: A | Deficient | Normal | Nutrition, dysphagia | Yes | Â |
13 | M | 14 | 4 | -4.42 | 22 | Yes: A | Deficient | Normal | Nutrition, dysphagia | Yes | Â |
14 | M | 16 | 4 | Â | 41 | Yes: A | Deficient | Normal | Nutrition, dysphagia | No | Leukemia, lung complications |
15 | M | 10 | 5 | -0.79 | 47 | Yes: A | Deficient | Deficient | Nutrition, dysphagia | No | Burkitt lymphoma; lung complications; recurrent aspiration |
16 | F | 12 | 5 | -7.57 | 39 | Yes: P | Deficient | Normal | Nutrition, dysphagia | No | Lung complications, failure to thrive, recurrent aspiration |
17 | M | 13 | 5 | -3.39 | 53 | Yes: P | Deficient | Deficient | Nutrition, dysphagia | Yes | Â |
18 | M | 15 | 6 | Â | Â | No | Deficient | Normal | Nutrition | No | Non-Hodgkin Lymphoma T cell |
19 | M | 17 | 6 | Â | Â | Yes: A, R | Deficient | Normal | Nutrition | No | Aspiration pneumonia |
20 | M | 5 | 8 | Â | Â | No | Normal | Deficient | Â | No | Hodgkin lymphoma |
21 | F | 11 | 8 | -3.12 | 35 | No | Normal | Normal | Nutrition | Yes | Â |
22 | M | 17 | 8 | -5.03 | 21 | Yes: P, R | Normal | Normal | Nutrition, dysphagia | No | T-Cell Lymphoma, lung complications |
23 | M | 7 | 9 | Â | Â | No | Deficient | Normal | Nutrition | Yes | Â |
24 | M | 15 | 9 | -11.89 | 19 | Yes: P | Deficient | Deficient | Â | No | Congestive heart failure |
25 | F | 6 | 11 | Â | Â | No | Deficient | Normal | Nutrition, recurrent lung infections | No | Congestive heart failure, lung disease |
Patients with early mortality following GT placement | |||||||||||
1 | F | 22 | 0 | -7.03 | 50 | Yes: P, R | Normal | Normal | Nutrition (10 lb weight loss/3 yrs), dysphagia, recurrent pneumonia | No | Did not tolerate GT feedings, pneumonia, and respiratory failure, |
2 | F | 25 | 0 | -1.10 | 53 | Yes: P | Not Done | Not Done | Nutrition (10 lb weight loss/1 yr), dysphagia, chronic cough, declining respiratory function (FVC = 20% predicted) | No | Did not tolerate GT feedings, pneumothorax, and respiratory failure |
3 | M | 27 | 0 | -7.78 | 15 | Yes: P, R | Deficient | Normal | Nutrition (16 lb weight loss/1 yr), dysphagia | No | Did not tolerate GT feedings, pneumonia, pneumothorax, and respiratory failure |